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@ARTICLE{Fluhrer:136438,
author = {Fluhrer, Regina and Martin, Lucas and Klier, Bärbel and
Haug-Kröper, Martina and Grammer, Gudula and Nuscher,
Brigitte and Haass, Christian},
title = {{T}he α-helical content of the transmembrane domain of the
{B}ritish dementia protein-2 ({B}ri2) determines its
processing by signal peptide peptidase-like 2b ({SPPL}2b).},
journal = {The journal of biological chemistry},
volume = {287},
number = {7},
issn = {0021-9258},
address = {Bethesda, Md.},
publisher = {Soc.60645},
reportid = {DZNE-2020-02760},
pages = {5156-5163},
year = {2012},
abstract = {Regulated intramembrane proteolysis is a widely accepted
concept describing the processing of various transmembrane
proteins via ectodomain shedding followed by an
intramembrane cleavage. The resulting cleavage products can
be involved in reverse signaling. Presenilins, which
constitute the active center of the γ-secretase complex,
signal peptide peptidase (SPP), and its homologues, the
SPP-like (SPPL) proteases are members of the family of
intramembrane-cleaving aspartyl proteases of the GXGD-type.
We recently demonstrated that Bri2 (itm2b) is a substrate
for regulated intramembrane proteolysis by SPPL2a and
SPPL2b. Intramembrane cleavage of Bri2 is triggered by an
initial shedding event catalyzed by A Disintegrin and
Metalloprotease 10 (ADAM10). Additionally primary sequence
determinants within the intracellular domain, the
transmembrane domain and the luminal juxtamembrane domain
are required for efficient cleavage of Bri2 by SPPL2b. Using
mutagenesis and circular dichroism spectroscopy we now
demonstrate that a high α-helical content of the Bri2
transmembrane domain (TMD) reduces cleavage efficiency of
Bri2 by SPPL2b, while the presence of a GXXXG dimerization
motif influences the intramembrane cleavage only to a minor
extent. Surprisingly, only one of the four conserved
intramembrane glycine residues significantly affects the
secondary structure of the Bri2 TMD and thereby its
intramembrane cleavage. Other glycine residues do not
influence the α-helical content of the transmembrane domain
nor its intramembrane processing.},
keywords = {ADAM Proteins: genetics / ADAM Proteins: metabolism /
ADAM10 Protein / Amino Acid Motifs / Amyloid Precursor
Protein Secretases: genetics / Amyloid Precursor Protein
Secretases: metabolism / Aspartic Acid Endopeptidases:
genetics / Aspartic Acid Endopeptidases: metabolism /
Circular Dichroism: methods / HEK293 Cells / Humans /
Membrane Glycoproteins / Membrane Proteins: genetics /
Membrane Proteins: metabolism / Mutagenesis / Protein
Structure, Tertiary / Proteolysis / ITM2B protein, human
(NLM Chemicals) / Membrane Glycoproteins (NLM Chemicals) /
Membrane Proteins (NLM Chemicals) / Amyloid Precursor
Protein Secretases (NLM Chemicals) / Aspartic Acid
Endopeptidases (NLM Chemicals) / SPPL2b protein, human (NLM
Chemicals) / ADAM Proteins (NLM Chemicals) / ADAM10 Protein
(NLM Chemicals) / ADAM10 protein, human (NLM Chemicals)},
cin = {AG Fluhrer / AG Haass old},
ddc = {540},
cid = {I:(DE-2719)1110000-2 / I:(DE-2719)1110007},
pnm = {342 - Disease Mechanisms and Model Systems (POF3-342)},
pid = {G:(DE-HGF)POF3-342},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:22194595},
pmc = {pmc:PMC3281599},
doi = {10.1074/jbc.M111.328104},
url = {https://pub.dzne.de/record/136438},
}