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000136455 0247_ $$2doi$$a10.1007/128_2011_160
000136455 0247_ $$2pmid$$apmid:21598098
000136455 0247_ $$2ISSN$$a0340-1022
000136455 0247_ $$2ISSN$$a1436-5049
000136455 037__ $$aDZNE-2020-02777
000136455 041__ $$aEnglish
000136455 082__ $$a540
000136455 1001_ $$0P:(DE-HGF)0$$aResenberger, Ulrike K$$b0
000136455 245__ $$aNeuroprotective and neurotoxic signaling by the prion protein.
000136455 260__ $$aHeidelberg$$bSpringer$$c2011
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000136455 29510 $$aPrion Proteins / Tatzelt, Jörg (Editor)   ; Berlin, Heidelberg : Springer Berlin Heidelberg, 2012, Chapter 160 ; ISSN: 0340-1022=1436-5049 ; ISBN: 978-3-642-24066-9=978-3-642-24067-6 ; doi:10.1007/978-3-642-24067-6
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000136455 4900_ $$aTopics in Current Chemistry$$v305
000136455 520__ $$aPrion diseases in humans and animals are characterized by progressive neurodegeneration and the formation of infectious particles called prions. Both features are intimately linked to a conformational transition of the cellular prion protein (PrP(C)) into aberrantly folded conformers with neurotoxic and self-replicating activities. Interestingly, there is increasing evidence that the infectious and neurotoxic properties of PrP conformers are not necessarily coupled. Transgenic mouse models revealed that some PrP mutants interfere with neuronal function in the absence of infectious prions. Vice versa, propagation of prions can occur without causing neurotoxicity. Consequently, it appears plausible that two partially independent pathways exist, one pathway leading to the propagation of infectious prions and another one that mediates neurotoxic signaling. In this review we will summarize current knowledge of neurotoxic PrP conformers and discuss the role of PrP(C) as a mediator of both stress-protective and neurotoxic signaling cascades.
000136455 536__ $$0G:(DE-HGF)POF3-341$$a341 - Molecular Signaling (POF3-341)$$cPOF3-341$$fPOF III$$x0
000136455 536__ $$0G:(DE-HGF)POF3-342$$a342 - Disease Mechanisms and Model Systems (POF3-342)$$cPOF3-342$$fPOF III$$x1
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000136455 650_7 $$2NLM Chemicals$$aPrions
000136455 650_2 $$2MeSH$$aAnimals
000136455 650_2 $$2MeSH$$aHumans
000136455 650_2 $$2MeSH$$aMice
000136455 650_2 $$2MeSH$$aModels, Biological
000136455 650_2 $$2MeSH$$aMutation
000136455 650_2 $$2MeSH$$aNeurodegenerative Diseases: metabolism
000136455 650_2 $$2MeSH$$aNeurons: metabolism
000136455 650_2 $$2MeSH$$aNeurons: pathology
000136455 650_2 $$2MeSH$$aNeurotoxicity Syndromes: metabolism
000136455 650_2 $$2MeSH$$aPrion Diseases: metabolism
000136455 650_2 $$2MeSH$$aPrion Diseases: pathology
000136455 650_2 $$2MeSH$$aPrions: metabolism
000136455 650_2 $$2MeSH$$aProtein Conformation
000136455 650_2 $$2MeSH$$aProtein Denaturation
000136455 650_2 $$2MeSH$$aProtein Folding
000136455 650_2 $$2MeSH$$aProtein Structure, Tertiary
000136455 650_2 $$2MeSH$$aSignal Transduction
000136455 7001_ $$0P:(DE-2719)9000369$$aWinklhofer, Konstanze F$$b1$$udzne
000136455 7001_ $$0P:(DE-2719)9000396$$aTatzelt, Jörg$$b2$$eLast author$$udzne
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000136455 9131_ $$0G:(DE-HGF)POF3-342$$1G:(DE-HGF)POF3-340$$2G:(DE-HGF)POF3-300$$aDE-HGF$$bForschungsbereich Gesundheit$$lErkrankungen des Nervensystems$$vDisease Mechanisms and Model Systems$$x1
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000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1111/j.1471-4159.2006.03906.x$$o10.1111/j.1471-4159.2006.03906.x
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1093/emboj/cdf324$$o10.1093/emboj/cdf324
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1093/emboj/cdf325$$o10.1093/emboj/cdf325
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/nm1297-1376$$o10.1038/nm1297-1376
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1523/JNEUROSCI.2313-05.2005$$o10.1523/JNEUROSCI.2313-05.2005
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1523/JNEUROSCI.1701-08.2008$$o10.1523/JNEUROSCI.1701-08.2008
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1002/glia.20861$$o10.1002/glia.20861
000136455 999C5 $$2Crossref$$oVR Martins 2010$$y2010
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1128/MCB.13.2.869$$o10.1128/MCB.13.2.869
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1074/jbc.272.3.1876$$o10.1074/jbc.272.3.1876
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1242/jcs.00905$$o10.1242/jcs.00905
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1111/j.1471-4159.2007.04904.x$$o10.1111/j.1471-4159.2007.04904.x
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1002/bies.200800151$$o10.1002/bies.200800151
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1074/jbc.M007114200$$o10.1074/jbc.M007114200
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.051627998$$o10.1073/pnas.051627998
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.251550798$$o10.1073/pnas.251550798
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1093/emboj/20.4.694$$o10.1093/emboj/20.4.694
000136455 999C5 $$2Crossref$$oN Nishida 1999$$y1999
000136455 999C5 $$2Crossref$$oGL Silverman 2000$$y2000
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1126/science.1094273$$o10.1126/science.1094273
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1152/physrev.00023.2009$$o10.1152/physrev.00023.2009
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/nn.2583$$o10.1038/nn.2583
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1007/s004010000271$$o10.1007/s004010000271
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1046/j.1365-2990.2000.00239.x$$o10.1046/j.1365-2990.2000.00239.x
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1007/s004010050870$$o10.1007/s004010050870
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1007/BF00713522$$o10.1007/BF00713522
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1002/ana.10507$$o10.1002/ana.10507
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.neurobiolaging.2004.10.004$$o10.1016/j.neurobiolaging.2004.10.004
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.0609621104$$o10.1073/pnas.0609621104
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/nature07761$$o10.1038/nature07761
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1074/jbc.M110.145516$$o10.1074/jbc.M110.145516
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1002/emmm.201000082$$o10.1002/emmm.201000082
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.0911829107$$o10.1073/pnas.0911829107
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1523/JNEUROSCI.0395-10.2010$$o10.1523/JNEUROSCI.0395-10.2010
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/nature09217$$o10.1038/nature09217
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1186/1471-2202-11-130$$o10.1186/1471-2202-11-130
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.neuron.2010.04.031$$o10.1016/j.neuron.2010.04.031
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/nrd2896$$o10.1038/nrd2896
000136455 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/emboj.2011.86$$o10.1038/emboj.2011.86
000136455 999C5 $$2Crossref$$oMF Tuite 2011$$y2011
000136455 999C5 $$2Crossref$$oD Westaway 2011$$y2011