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000136463 0247_ $$2doi$$a10.1007/s00401-011-0902-3
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000136463 0247_ $$2ISSN$$a1432-0533
000136463 037__ $$aDZNE-2020-02785
000136463 041__ $$aEnglish
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000136463 1001_ $$0P:(DE-2719)9000909$$aPilsl, Anna$$b0$$eFirst author$$udzne
000136463 245__ $$aParkin, PINK1 and mitochondrial integrity: emerging concepts of mitochondrial dysfunction in Parkinson's disease.
000136463 260__ $$aHeidelberg$$bSpringer$$c2012
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000136463 520__ $$aMitochondria are dynamic organelles which are essential for many cellular processes, such as ATP production by oxidative phosphorylation, lipid metabolism, assembly of iron sulfur clusters, regulation of calcium homeostasis, and cell death pathways. The dynamic changes in mitochondrial morphology, connectivity, and subcellular distribution are critically dependent on a highly regulated fusion and fission machinery. Mitochondrial function, dynamics, and quality control are vital for the maintenance of neuronal integrity. Indeed, there is mounting evidence that mitochondrial dysfunction plays a central role in several neurodegenerative diseases. In particular, the identification of genes linked to rare familial variants of Parkinson's disease has fueled research on mitochondrial aspects of the disease etiopathogenesis. Studies on the function of parkin and PINK1, which are associated with autosomal recessive parkinsonism, provided compelling evidence that these proteins can functionally interact to maintain mitochondrial integrity and to promote clearance of damaged and dysfunctional mitochondria. In this review we will summarize current knowledge about the impact of parkin and PINK1 on mitochondria.
000136463 536__ $$0G:(DE-HGF)POF3-341$$a341 - Molecular Signaling (POF3-341)$$cPOF3-341$$fPOF III$$x0
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000136463 650_7 $$2NLM Chemicals$$aMitochondrial Proteins
000136463 650_7 $$0EC 2.3.2.27$$2NLM Chemicals$$aUbiquitin-Protein Ligases
000136463 650_7 $$0EC 2.3.2.27$$2NLM Chemicals$$aparkin protein
000136463 650_7 $$0EC 2.7.-$$2NLM Chemicals$$aProtein Kinases
000136463 650_7 $$0EC 2.7.11.1$$2NLM Chemicals$$aPTEN-induced putative kinase
000136463 650_2 $$2MeSH$$aAnimals
000136463 650_2 $$2MeSH$$aHumans
000136463 650_2 $$2MeSH$$aMitochondrial Diseases: genetics
000136463 650_2 $$2MeSH$$aMitochondrial Diseases: metabolism
000136463 650_2 $$2MeSH$$aMitochondrial Diseases: physiopathology
000136463 650_2 $$2MeSH$$aMitochondrial Proteins: genetics
000136463 650_2 $$2MeSH$$aMitochondrial Proteins: physiology
000136463 650_2 $$2MeSH$$aParkinson Disease: genetics
000136463 650_2 $$2MeSH$$aParkinson Disease: metabolism
000136463 650_2 $$2MeSH$$aParkinson Disease: physiopathology
000136463 650_2 $$2MeSH$$aParkinsonian Disorders: genetics
000136463 650_2 $$2MeSH$$aParkinsonian Disorders: metabolism
000136463 650_2 $$2MeSH$$aParkinsonian Disorders: physiopathology
000136463 650_2 $$2MeSH$$aProtein Kinases: genetics
000136463 650_2 $$2MeSH$$aProtein Kinases: physiology
000136463 650_2 $$2MeSH$$aUbiquitin-Protein Ligases: genetics
000136463 650_2 $$2MeSH$$aUbiquitin-Protein Ligases: physiology
000136463 7001_ $$0P:(DE-2719)9000369$$aWinklhofer, Konstanze F$$b1$$eLast author$$udzne
000136463 77318 $$2Crossref$$3journal-article$$a10.1007/s00401-011-0902-3$$b : Springer Science and Business Media LLC, 2011-11-06$$n2$$p173-188$$tActa Neuropathologica$$v123$$x0001-6322$$y2011
000136463 773__ $$0PERI:(DE-600)1458410-4$$a10.1007/s00401-011-0902-3$$gVol. 123, no. 2, p. 173 - 188$$n2$$p173-188$$q123:2<173 - 188$$tActa neuropathologica$$v123$$x0001-6322$$y2012
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000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1083/jcb.200809125$$o10.1083/jcb.200809125
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1371/journal.pbio.1000298$$o10.1371/journal.pbio.1000298
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/0024-3205(85)90146-8$$o10.1016/0024-3205(85)90146-8
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1002/humu.21277$$o10.1002/humu.21277
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/nm.2165$$o10.1038/nm.2165
000136463 999C5 $$2Crossref$$oK Okatsu 2010$$y2010
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1074/jbc.M401135200$$o10.1074/jbc.M401135200
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.bbrc.2008.11.086$$o10.1016/j.bbrc.2008.11.086
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/nature04788$$o10.1038/nature04788
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/S0896-6273(02)01125-X$$o10.1016/S0896-6273(02)01125-X
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/ncb1644$$o10.1038/ncb1644
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.0709336105$$o10.1073/pnas.0709336105
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1371/journal.pone.0010054$$o10.1371/journal.pone.0010054
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1371/journal.pbio.0050172$$o10.1371/journal.pbio.0050172
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.93.10.4565$$o10.1073/pnas.93.10.4565
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.1107402108$$o10.1073/pnas.1107402108
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.febslet.2007.11.034$$o10.1016/j.febslet.2007.11.034
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1074/jbc.M512649200$$o10.1074/jbc.M512649200
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1371/journal.pone.0005701$$o10.1371/journal.pone.0005701
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/ng.485$$o10.1038/ng.485
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.bbamcr.2010.09.019$$o10.1016/j.bbamcr.2010.09.019
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/S1474-4422(07)70327-7$$o10.1016/S1474-4422(07)70327-7
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/S0140-6736(89)92366-0$$o10.1016/S0140-6736(89)92366-0
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1074/jbc.M707494200$$o10.1074/jbc.M707494200
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.neuron.2011.06.003$$o10.1016/j.neuron.2011.06.003
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1523/JNEUROSCI.4441-10.2011$$o10.1523/JNEUROSCI.4441-10.2011
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1093/hmg/ddp501$$o10.1093/hmg/ddp501
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1093/hmg/ddr077$$o10.1093/hmg/ddr077
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.bbrc.2009.04.006$$o10.1016/j.bbrc.2009.04.006
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.cell.2011.02.010$$o10.1016/j.cell.2011.02.010
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1146/annurev-pathol-011110-130242$$o10.1146/annurev-pathol-011110-130242
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1093/hmg/ddi377$$o10.1093/hmg/ddi377
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/ng.487$$o10.1038/ng.487
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.bbamcr.2008.07.008$$o10.1016/j.bbamcr.2008.07.008
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/42166$$o10.1038/42166
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/S0896-6273(03)00084-9$$o10.1016/S0896-6273(03)00084-9
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.1103295108$$o10.1073/pnas.1103295108
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/cdd.2009.23$$o10.1038/cdd.2009.23
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.neulet.2007.10.019$$o10.1016/j.neulet.2007.10.019
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1007/s00439-005-0038-4$$o10.1007/s00439-005-0038-4
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1083/jcb.201007013$$o10.1083/jcb.201007013
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/sj.emboj.7601972$$o10.1038/sj.emboj.7601972
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1111/j.1742-4658.2008.06302.x$$o10.1111/j.1742-4658.2008.06302.x
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.biocel.2009.02.018$$o10.1016/j.biocel.2009.02.018
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/emboj.2009.89$$o10.1038/emboj.2009.89
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/sj.emboj.7601963$$o10.1038/sj.emboj.7601963
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.expneurol.2008.04.026$$o10.1016/j.expneurol.2008.04.026
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.mcn.2008.12.010$$o10.1016/j.mcn.2008.12.010
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1126/science.1096284$$o10.1126/science.1096284
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1523/JNEUROSCI.1917-11.2011$$o10.1523/JNEUROSCI.1917-11.2011
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1093/hmg/ddq531$$o10.1093/hmg/ddq531
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.expneurol.2009.03.019$$o10.1016/j.expneurol.2009.03.019
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1111/j.1471-4159.2008.05604.x$$o10.1111/j.1471-4159.2008.05604.x
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.0911187107$$o10.1073/pnas.0911187107
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.neuron.2011.08.033$$o10.1016/j.neuron.2011.08.033
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1093/hmg/ddi413$$o10.1093/hmg/ddi413
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1074/jbc.M110.144238$$o10.1074/jbc.M110.144238
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1093/hmg/ddm334$$o10.1093/hmg/ddm334
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1021/bi8019178$$o10.1021/bi8019178
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1002/iub.261$$o10.1002/iub.261
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1242/dmm.000109$$o10.1242/dmm.000109
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1517/14728222.11.12.1543$$o10.1517/14728222.11.12.1543
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.bbadis.2009.08.013$$o10.1016/j.bbadis.2009.08.013
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1074/jbc.M306769200$$o10.1074/jbc.M306769200
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/sj.emboj.7601930$$o10.1038/sj.emboj.7601930
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1074/jbc.M609466200$$o10.1074/jbc.M609466200
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1371/journal.pone.0002455$$o10.1371/journal.pone.0002455
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.bbabio.2009.02.005$$o10.1016/j.bbabio.2009.02.005
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.0602493103$$o10.1073/pnas.0602493103
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.0711845105$$o10.1073/pnas.0711845105
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/ncb0910-814$$o10.1038/ncb0910-814
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.0404161101$$o10.1073/pnas.0404161101
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1074/jbc.M110.209338$$o10.1074/jbc.M110.209338
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1523/JNEUROSCI.5141-08.2008$$o10.1523/JNEUROSCI.5141-08.2008
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.0802814105$$o10.1073/pnas.0802814105
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.7150/ijbs.3.242$$o10.7150/ijbs.3.242
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1073/pnas.0913485107$$o10.1073/pnas.0913485107
000136463 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/ng1341$$o10.1038/ng1341