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@ARTICLE{Synofzik:137248,
author = {Synofzik, Matthis and Bernard, Geneviève and Lindig,
Tobias and Gburek-Augustat, Janina},
title = {{T}eaching neuroimages: hypomyelinating leukodystrophy with
hypodontia due to {POLR}3{B}: look into a leukodystrophy's
mouth.},
journal = {Neurology},
volume = {81},
number = {19},
issn = {0028-3878},
address = {[S.l.]},
publisher = {Ovid},
reportid = {DZNE-2020-03570},
pages = {e145-e145},
year = {2013},
abstract = {An 18-year-old German woman presented with progressive
cerebellar ataxia since early childhood, delayed cognitive
development, and hypogonadotropic hypogonadism. MRI
demonstrated diffuse cerebral hypomyelination, cerebellar
atrophy, and thin corpus callosum; X-ray revealed persistent
milk teeth and hypoplastic crowns and roots (figure),
indicative of 4H syndrome (hypomyelination, hypodontia,
hypogonadotropic hypogonadism). POLR3B sequencing(1)
revealed 2 compound heterozygous mutations (C527R
[C.1579T>C] and the common ancestral V523E [C.1568T>A](2)).},
subtyp = {Editorial},
keywords = {Adolescent / Anodontia: complications / Anodontia: genetics
/ Anodontia: pathology / Female / Hereditary Central Nervous
System Demyelinating Diseases: complications / Hereditary
Central Nervous System Demyelinating Diseases: genetics /
Hereditary Central Nervous System Demyelinating Diseases:
pathology / Humans / Magnetic Resonance Imaging / Mouth:
pathology / RNA Polymerase III: genetics / POLR3B protein,
human (NLM Chemicals) / RNA Polymerase III (NLM Chemicals)},
cin = {AG Gasser 1},
ddc = {610},
cid = {I:(DE-2719)1210000},
pnm = {345 - Population Studies and Genetics (POF3-345)},
pid = {G:(DE-HGF)POF3-345},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:24190003},
pmc = {pmc:PMC3812106},
doi = {10.1212/01.wnl.0000435300.64776.7e},
url = {https://pub.dzne.de/record/137248},
}