TY - JOUR AU - Kraft, Peter AU - Schuhmann, Michael K AU - Garz, Cornelia AU - Jandke, Solveig AU - Urlaub, Daniela AU - Mencl, Stine AU - Zernecke, Alma AU - Heinze, Hans-Jochen AU - Carare, Roxana O AU - Kleinschnitz, Christoph AU - Schreiber, Stefanie TI - Hypercholesterolemia induced cerebral small vessel disease. JO - PLOS ONE VL - 12 IS - 8 SN - 1932-6203 CY - San Francisco, California, US PB - PLOS M1 - DZNE-2020-05764 SP - e0182822 PY - 2017 AB - BackgroundWhile hypercholesterolemia plays a causative role for the development of ischemic stroke in large vessels, its significance for cerebral small vessel disease (CSVD) remains unclear. We thus aimed to understand the detailed relationship between hypercholesterolemia and CSVD using the well described Ldlr-/- mouse model.MethodsWe used Ldlr-/- mice (n = 16) and wild-type (WT) mice (n = 15) at the age of 6 and 12 months. Ldlr-/- mice develop high plasma cholesterol levels following a high fat diet. We analyzed cerebral capillaries and arterioles for intravascular erythrocyte accumulations, thrombotic vessel occlusions, blood-brain barrier (BBB) dysfunction and microbleeds.ResultsWe found a significant increase in the number of erythrocyte stases in 6 months old Ldlr-/- mice compared to all other groups (P < 0.05). Ldlr-/- animals aged 12 months showed the highest number of thrombotic occlusions while in WT animals hardly any occlusions could be observed (P < 0.001). Compared to WT mice, Ldlr-/- mice did not display significant gray matter BBB breakdown. Microhemorrhages were observed in one Ldlr-/- mouse that was 6 months old. Results did not differ when considering subcortical and cortical regions.ConclusionsIn Ldlr-/- mice, hypercholesterolemia is related to a thrombotic CSVD phenotype, which is different from hypertension-related CSVD that associates with a hemorrhagic CSVD phenotype. Our data demonstrate a relationship between hypercholesterolemia and the development of CSVD. Ldlr-/- mice appear to be an adequate animal model for research into CSVD. KW - Animals KW - Blood-Brain Barrier: physiopathology KW - Brain: physiopathology KW - Cerebral Small Vessel Diseases: blood KW - Cerebral Small Vessel Diseases: etiology KW - Cerebral Small Vessel Diseases: genetics KW - Cerebral Small Vessel Diseases: physiopathology KW - Cholesterol: blood KW - Diet, High-Fat KW - Disease Models, Animal KW - Hypercholesterolemia: blood KW - Hypercholesterolemia: complications KW - Hypercholesterolemia: genetics KW - Hypercholesterolemia: physiopathology KW - Male KW - Mice KW - Mice, Knockout KW - Receptors, LDL: genetics KW - Receptors, LDL (NLM Chemicals) KW - Cholesterol (NLM Chemicals) LB - PUB:(DE-HGF)16 C6 - pmid:28796818 C2 - pmc:PMC5552130 DO - DOI:10.1371/journal.pone.0182822 UR - https://pub.dzne.de/record/139442 ER -