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000140231 1001_ $$0P:(DE-2719)2000010$$aJucker, Mathias$$b0$$eFirst author
000140231 245__ $$aPropagation and spread of pathogenic protein assemblies in neurodegenerative diseases.
000140231 260__ $$aLondon$$bNature Publ. Group58142$$c2018
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000140231 520__ $$aMany neurodegenerative diseases, such as Alzheimer's disease, Parkinson's disease, and amyotrophic lateral sclerosis, are characterized by the progressive appearance of abnormal proteinaceous assemblies in the nervous system. Studies in experimental systems indicate that the assemblies originate from the prion-like seeded aggregation of specific misfolded proteins that proliferate and amass to form the intracellular and/or extracellular lesions typical of each disorder. The host in which the proteopathic seeds arise provides the biochemical and physiological environment that either supports or restricts their emergence, proliferation, self-assembly, and spread. Multiple mechanisms influence the spatiotemporal spread of seeds and the nature of the resulting lesions, one of which is the cellular uptake, release, and transport of seeds along neural pathways and networks. The characteristics of cells and regions in the affected network govern their vulnerability and thereby influence the neuropathological and clinical attributes of the disease. The propagation of pathogenic protein assemblies within the nervous system is thus determined by the interaction of the proteopathic agent and the host milieu.
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000140231 650_7 $$2NLM Chemicals$$aPrions
000140231 650_2 $$2MeSH$$aAnimals
000140231 650_2 $$2MeSH$$aCell Communication
000140231 650_2 $$2MeSH$$aHumans
000140231 650_2 $$2MeSH$$aNeurodegenerative Diseases: metabolism
000140231 650_2 $$2MeSH$$aNeurodegenerative Diseases: pathology
000140231 650_2 $$2MeSH$$aPrions: metabolism
000140231 650_2 $$2MeSH$$aPrions: pathogenicity
000140231 7001_ $$0P:(DE-2719)9000947$$aWalker, Lary C$$b1$$eLast author
000140231 77318 $$2Crossref$$3journal-article$$a10.1038/s41593-018-0238-6$$b : Springer Science and Business Media LLC, 2018-09-26$$n10$$p1341-1349$$tNature Neuroscience$$v21$$x1097-6256$$y2018
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000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1146/annurev-biochem-060614-033955$$o10.1146/annurev-biochem-060614-033955
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1523/JNEUROSCI.1787-16.2017$$o10.1523/JNEUROSCI.1787-16.2017
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1136/jnnp-2015-311321$$o10.1136/jnnp-2015-311321
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1007/s00401-018-1829-8$$o10.1007/s00401-018-1829-8
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.3389/fneur.2017.00653$$o10.3389/fneur.2017.00653
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1074/jbc.M115.681791$$o10.1074/jbc.M115.681791
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1126/sciadv.1600947$$o10.1126/sciadv.1600947
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1186/2051-5960-2-8$$o10.1186/2051-5960-2-8
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1126/science.aah3374$$o10.1126/science.aah3374
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/ncb3372$$o10.1038/ncb3372
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.celrep.2018.04.056$$o10.1016/j.celrep.2018.04.056
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.15252/embr.201744067$$o10.15252/embr.201744067
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/nn.2801$$o10.1038/nn.2801
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1084/jem.20131685$$o10.1084/jem.20131685
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1186/s13024-018-0241-0$$o10.1186/s13024-018-0241-0
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1523/JNEUROSCI.19-19-08552.1999$$o10.1523/JNEUROSCI.19-19-08552.1999
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/nn.4132$$o10.1038/nn.4132
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1016/j.cell.2017.05.018$$o10.1016/j.cell.2017.05.018
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/nature25158$$o10.1038/nature25158
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.3389/fnins.2018.00267$$o10.3389/fnins.2018.00267
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1007/s00401-018-1855-6$$o10.1007/s00401-018-1855-6
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1038/nature14377$$o10.1038/nature14377
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1002/ana.24174$$o10.1002/ana.24174
000140231 999C5 $$2Crossref$$9-- missing cx lookup --$$a10.1007/s00401-016-1582-9$$o10.1007/s00401-016-1582-9