000140673 001__ 140673 000140673 005__ 20240321220843.0 000140673 0247_ $$2doi$$a10.1016/j.jmb.2019.01.019 000140673 0247_ $$2pmid$$apmid:30664869 000140673 0247_ $$2ISSN$$a0022-2836 000140673 0247_ $$2ISSN$$a1089-8638 000140673 0247_ $$2altmetric$$aaltmetric:70432503 000140673 037__ $$aDZNE-2020-06995 000140673 041__ $$aEnglish 000140673 082__ $$a610 000140673 1001_ $$0P:(DE-2719)2421562$$aKrauss, Sybille$$b0$$eFirst author$$udzne 000140673 245__ $$aThe Role of MicroRNAs in Spinocerebellar Ataxia Type 3. 000140673 260__ $$aAmsterdam [u.a.]$$bElsevier$$c2019 000140673 264_1 $$2Crossref$$3print$$bElsevier BV$$c2019-04-01 000140673 3367_ $$2DRIVER$$aarticle 000140673 3367_ $$2DataCite$$aOutput Types/Journal article 000140673 3367_ $$0PUB:(DE-HGF)16$$2PUB:(DE-HGF)$$aJournal Article$$bjournal$$mjournal$$s1685012194_32156$$xReview Article 000140673 3367_ $$2BibTeX$$aARTICLE 000140673 3367_ $$2ORCID$$aJOURNAL_ARTICLE 000140673 3367_ $$00$$2EndNote$$aJournal Article 000140673 520__ $$aMore than 90% of the human genome are transcribed as non-coding RNAs. While it is still under debate if all these non-coding transcripts are functional, there is emerging evidence that RNA has several important functions in addition to coding for proteins. For example, microRNAs (miRNAs) are important regulatory RNAs that control gene expression in various biological processes and human diseases. In spinocerebellar ataxia type 3 (SCA3), a devastating neurodegenerative disease, miRNAs are involved in the disease process at different levels, including the deregulation of components of the general miRNA biogenesis machinery, as well as in the cell type-specific control of the expression of the SCA3 disease protein and other SCA3 disease-relevant proteins. However, it remains difficult to predict whether these changes are a cause or a consequence of the neurodegenerative process in SCA3. Further studies using standardized procedures for the analysis of miRNA expression and larger sample numbers are required to enhance our understanding of the miRNA-mediated processes involved in SCA3 disease and may enable the development of miRNA-based therapeutics. In this review, we summarize the findings of independent studies highlighting both the disease-related and cytoprotective roles of miRNAs that have been implicated so far in the disease process of SCA3. 000140673 536__ $$0G:(DE-HGF)POF3-342$$a342 - Disease Mechanisms and Model Systems (POF3-342)$$cPOF3-342$$fPOF III$$x0 000140673 542__ $$2Crossref$$i2019-04-01$$uhttps://www.elsevier.com/tdm/userlicense/1.0/ 000140673 542__ $$2Crossref$$i2019-01-30$$uhttp://creativecommons.org/licenses/by-nc-nd/4.0/ 000140673 588__ $$aDataset connected to CrossRef, PubMed, 000140673 650_2 $$2MeSH$$aAnimals 000140673 650_2 $$2MeSH$$aAtaxin-3: genetics 000140673 650_2 $$2MeSH$$aAtaxin-3: metabolism 000140673 650_2 $$2MeSH$$aBiomarkers: metabolism 000140673 650_2 $$2MeSH$$aBrain: metabolism 000140673 650_2 $$2MeSH$$aBrain: pathology 000140673 650_2 $$2MeSH$$aCell Line 000140673 650_2 $$2MeSH$$aDisease Models, Animal 000140673 650_2 $$2MeSH$$aDrosophila melanogaster: genetics 000140673 650_2 $$2MeSH$$aDrosophila melanogaster: metabolism 000140673 650_2 $$2MeSH$$aGene Expression Regulation 000140673 650_2 $$2MeSH$$aHumans 000140673 650_2 $$2MeSH$$aLymphocytes: metabolism 000140673 650_2 $$2MeSH$$aLymphocytes: pathology 000140673 650_2 $$2MeSH$$aMachado-Joseph Disease: genetics 000140673 650_2 $$2MeSH$$aMachado-Joseph Disease: metabolism 000140673 650_2 $$2MeSH$$aMachado-Joseph Disease: pathology 000140673 650_2 $$2MeSH$$aMachado-Joseph Disease: therapy 000140673 650_2 $$2MeSH$$aMice 000140673 650_2 $$2MeSH$$aMicroRNAs: genetics 000140673 650_2 $$2MeSH$$aMicroRNAs: metabolism 000140673 650_2 $$2MeSH$$aMolecular Targeted Therapy: methods 000140673 650_2 $$2MeSH$$aNeurons: metabolism 000140673 650_2 $$2MeSH$$aNeurons: pathology 000140673 650_2 $$2MeSH$$aRepressor Proteins: genetics 000140673 650_2 $$2MeSH$$aRepressor Proteins: metabolism 000140673 650_2 $$2MeSH$$aSignal Transduction 000140673 7001_ $$0P:(DE-HGF)0$$aEvert, Bernd O$$b1$$eCorresponding author 000140673 77318 $$2Crossref$$3journal-article$$a10.1016/j.jmb.2019.01.019$$b : Elsevier BV, 2019-04-01$$n9$$p1729-1742$$tJournal of Molecular Biology$$v431$$x0022-2836$$y2019 000140673 773__ $$0PERI:(DE-600)1355192-9$$a10.1016/j.jmb.2019.01.019$$gVol. 431, no. 9, p. 1729 - 1742$$n9$$p1729-1742$$q431:9<1729 - 1742$$tJournal of molecular biology$$v431$$x0022-2836$$y2019 000140673 8564_ $$uhttps://pub.dzne.de/record/140673/files/DZNE-2020-06995.pdf$$yOpenAccess 000140673 8564_ $$uhttps://pub.dzne.de/record/140673/files/DZNE-2020-06995.pdf?subformat=pdfa$$xpdfa$$yOpenAccess 000140673 909CO $$ooai:pub.dzne.de:140673$$pdnbdelivery$$pdriver$$pVDB$$popen_access$$popenaire 000140673 9101_ $$0I:(DE-588)1065079516$$6P:(DE-2719)2421562$$aDeutsches Zentrum für Neurodegenerative Erkrankungen$$b0$$kDZNE 000140673 9131_ $$0G:(DE-HGF)POF3-342$$1G:(DE-HGF)POF3-340$$2G:(DE-HGF)POF3-300$$3G:(DE-HGF)POF3$$4G:(DE-HGF)POF$$aDE-HGF$$bGesundheit$$lErkrankungen des Nervensystems$$vDisease Mechanisms and Model Systems$$x0 000140673 9141_ $$y2019 000140673 915__ $$0LIC:(DE-HGF)CCBYNCND4$$2HGFVOC$$aCreative Commons Attribution-NonCommercial-NoDerivs CC BY-NC-ND 4.0 000140673 915__ $$0StatID:(DE-HGF)0510$$2StatID$$aOpenAccess 000140673 915__ $$0StatID:(DE-HGF)0420$$2StatID$$aNationallizenz$$d2022-11-08$$wger 000140673 915__ $$0StatID:(DE-HGF)0100$$2StatID$$aJCR$$bJ MOL BIOL : 2021$$d2022-11-08 000140673 915__ $$0StatID:(DE-HGF)0200$$2StatID$$aDBCoverage$$bSCOPUS$$d2022-11-08 000140673 915__ $$0StatID:(DE-HGF)0300$$2StatID$$aDBCoverage$$bMedline$$d2022-11-08 000140673 915__ $$0StatID:(DE-HGF)0600$$2StatID$$aDBCoverage$$bEbsco Academic Search$$d2022-11-08 000140673 915__ $$0StatID:(DE-HGF)0030$$2StatID$$aPeer Review$$bASC$$d2022-11-08 000140673 915__ $$0StatID:(DE-HGF)0199$$2StatID$$aDBCoverage$$bClarivate Analytics Master Journal List$$d2022-11-08 000140673 915__ $$0StatID:(DE-HGF)0150$$2StatID$$aDBCoverage$$bWeb of Science Core Collection$$d2022-11-08 000140673 915__ $$0StatID:(DE-HGF)1050$$2StatID$$aDBCoverage$$bBIOSIS Previews$$d2022-11-08 000140673 915__ $$0StatID:(DE-HGF)1030$$2StatID$$aDBCoverage$$bCurrent Contents - Life Sciences$$d2022-11-08 000140673 915__ $$0StatID:(DE-HGF)9905$$2StatID$$aIF >= 5$$bJ MOL BIOL : 2021$$d2022-11-08 000140673 9201_ $$0I:(DE-2719)1011006$$kAG Krauß ; AG Krauß$$lRegulatory RNA-protein interaction in neurodegenerative diseases$$x0 000140673 980__ $$ajournal 000140673 980__ $$aVDB 000140673 980__ $$aUNRESTRICTED 000140673 980__ $$aI:(DE-2719)1011006 000140673 9801_ $$aFullTexts