TY - JOUR
AU - Chiu, Celine
AU - Loth, Stefanie
AU - Kuhlen, Michaela
AU - Ginzel, Sebastian
AU - Schaper, Jörg
AU - Rosenbaum, Thorsten
AU - Pietsch, Torsten
AU - Borkhardt, Arndt
AU - Hoell, Jessica I
TI - Mutated SON putatively causes a cancer syndrome comprising high-risk medulloblastoma combined with café-au-lait spots.
JO - Familial cancer
VL - 18
IS - 3
SN - 1389-9600
CY - Dordrecht [u.a.]
PB - Springer Science + Business Media B.V
M1 - DZNE-2020-07071
SP - 353-358
PY - 2019
AB - Medulloblastoma is the most frequent malignant brain tumor in childhood. This highly malignant neoplasm occurs usually before 10 years of age and more frequently in boys. The 5-year event-free survival rate for high-risk medulloblastoma is low at 62
KW - Cafe-au-Lait Spots: genetics
KW - Cerebellar Neoplasms: genetics
KW - Child, Preschool
KW - Consanguinity
KW - DNA-Binding Proteins: genetics
KW - Fatal Outcome
KW - Humans
KW - Male
KW - Medulloblastoma: genetics
KW - Minor Histocompatibility Antigens: genetics
KW - Pedigree
KW - Point Mutation
KW - Syndrome
KW - DNA-Binding Proteins (NLM Chemicals)
KW - Minor Histocompatibility Antigens (NLM Chemicals)
KW - SON protein, human (NLM Chemicals)
LB - PUB:(DE-HGF)16
C6 - pmid:30680470
DO - DOI:10.1007/s10689-019-00121-z
UR - https://pub.dzne.de/record/140749
ER -