000144973 001__ 144973 000144973 005__ 20240813150347.0 000144973 0247_ $$2doi$$a10.1016/bs.irn.2019.10.013 000144973 0247_ $$2pmid$$apmid:31779824 000144973 0247_ $$2ISSN$$a0074-7742 000144973 0247_ $$2ISSN$$a2162-5514 000144973 0247_ $$2altmetric$$aaltmetric:71416658 000144973 037__ $$aDZNE-2020-00337 000144973 041__ $$aEnglish 000144973 082__ $$a610 000144973 1001_ $$0P:(DE-HGF)0$$aGiagkou, Nikolaos$$b0 000144973 245__ $$aProgressive supranuclear palsy. 000144973 260__ $$aHeidelberg [u.a.]$$bElsevier, Acad. Press$$c2019 000144973 264_1 $$2Crossref$$3print$$bElsevier$$c2019-01-01 000144973 3367_ $$2DRIVER$$aarticle 000144973 3367_ $$2DataCite$$aOutput Types/Journal article 000144973 3367_ $$0PUB:(DE-HGF)16$$2PUB:(DE-HGF)$$aJournal Article$$bjournal$$mjournal$$s1723554197_24566 000144973 3367_ $$2BibTeX$$aARTICLE 000144973 3367_ $$2ORCID$$aJOURNAL_ARTICLE 000144973 3367_ $$00$$2EndNote$$aJournal Article 000144973 520__ $$aProgressive supranuclear palsy (PSP) is a neurodegenerative disease characterized pathologically by 4 repeat tau deposition in various cell types and anatomical regions. Richardson's syndrome (RS) is the initially described and one of the clinical phenotypes associated with PSP pathology, characterized by vertical supranuclear gaze paly in particular downwards, postural instability with early falls and subcortical frontal dementia. PSP can manifest as several other clinical phenotypes, including PSP-parkinsonism, -pure akinesia with gait freezing, -frontotemporal dementia, - corticobasal syndrome, - speech/language impairment. RS can also have a pathologic diagnosis other than PSP, including corticobasal degeneration, FTD-TDP-43 and others. New clinical diagnostic criteria take into account this phenotypic variability in an attempt to diagnose the disease earlier, given the current lack of a validated biomarker. At present, therapeutic options for PSP are symptomatic and insufficient. Recent large neuroprotective trials have failed to provide a positive clinical outcome, however, have led to the design of better studies that are ongoing and hold promise for a neuroprotective treatment for PSP. 000144973 536__ $$0G:(DE-HGF)POF3-344$$a344 - Clinical and Health Care Research (POF3-344)$$cPOF3-344$$fPOF III$$x0 000144973 542__ $$2Crossref$$i2019-01-01$$uhttps://www.elsevier.com/tdm/userlicense/1.0/ 000144973 588__ $$aDataset connected to CrossRef Book Series, PubMed, 000144973 650_2 $$2MeSH$$aHumans 000144973 650_2 $$2MeSH$$aSupranuclear Palsy, Progressive: diagnosis 000144973 650_2 $$2MeSH$$aSupranuclear Palsy, Progressive: drug therapy 000144973 650_2 $$2MeSH$$aSupranuclear Palsy, Progressive: metabolism 000144973 650_2 $$2MeSH$$aSupranuclear Palsy, Progressive: physiopathology 000144973 7001_ $$0P:(DE-2719)2811373$$aHöglinger, Günter U$$b1$$udzne 000144973 7001_ $$0P:(DE-HGF)0$$aStamelou, Maria$$b2$$eCorresponding author 000144973 77318 $$2Crossref$$3book-chapter$$a10.1016/bs.irn.2019.10.013$$b : Elsevier, 2019-01-01$$p49-86$$tInternational Review of Neurobiology$$x0074-7742$$y2019 000144973 773__ $$0PERI:(DE-600)209876-3$$a10.1016/bs.irn.2019.10.013$$p49-86$$tInternational review of neurobiology$$v149$$x0074-7742$$y2019 000144973 8564_ $$uhttps://pub.dzne.de/record/144973/files/DZNE-2020-00337_Restricted.pdf 000144973 8564_ $$uhttps://pub.dzne.de/record/144973/files/DZNE-2020-00337_Restricted.pdf?subformat=pdfa$$xpdfa 000144973 909CO $$ooai:pub.dzne.de:144973$$pVDB 000144973 9101_ $$0I:(DE-588)1065079516$$6P:(DE-2719)2811373$$aDeutsches Zentrum für Neurodegenerative Erkrankungen$$b1$$kDZNE 000144973 9131_ $$0G:(DE-HGF)POF3-344$$1G:(DE-HGF)POF3-340$$2G:(DE-HGF)POF3-300$$3G:(DE-HGF)POF3$$4G:(DE-HGF)POF$$aDE-HGF$$bGesundheit$$lErkrankungen des Nervensystems$$vClinical and Health Care Research$$x0 000144973 9141_ $$y2019 000144973 915__ $$0StatID:(DE-HGF)0200$$2StatID$$aDBCoverage$$bSCOPUS 000144973 915__ $$0StatID:(DE-HGF)0300$$2StatID$$aDBCoverage$$bMedline 000144973 915__ $$0StatID:(DE-HGF)0310$$2StatID$$aDBCoverage$$bNCBI Molecular Biology Database 000144973 915__ $$0StatID:(DE-HGF)0199$$2StatID$$aDBCoverage$$bClarivate Analytics Master Journal List 000144973 915__ $$0StatID:(DE-HGF)0110$$2StatID$$aWoS$$bScience Citation Index 000144973 915__ $$0StatID:(DE-HGF)0150$$2StatID$$aDBCoverage$$bWeb of Science Core Collection 000144973 915__ $$0StatID:(DE-HGF)0111$$2StatID$$aWoS$$bScience Citation Index Expanded 000144973 915__ $$0StatID:(DE-HGF)1050$$2StatID$$aDBCoverage$$bBIOSIS Previews 000144973 915__ $$0StatID:(DE-HGF)1120$$2StatID$$aDBCoverage$$bBIOSIS Reviews Reports And Meetings 000144973 9201_ $$0I:(DE-2719)1110002$$kAG Höglinger 1 ; AG Höglinger$$lTranslational Neurodegeneration$$x0 000144973 980__ $$ajournal 000144973 980__ $$aVDB 000144973 980__ $$aI:(DE-2719)1110002 000144973 980__ $$aUNRESTRICTED