TY - JOUR
AU - Caporali, Leonardo
AU - Magri, Stefania
AU - Legati, Andrea
AU - Del Dotto, Valentina
AU - Tagliavini, Francesca
AU - Balistreri, Francesca
AU - Nasca, Alessia
AU - La Morgia, Chiara
AU - Carbonelli, Michele
AU - Valentino, Maria L.
AU - Lamantea, Eleonora
AU - Baratta, Silvia
AU - Schöls, Ludger
AU - Schüle, Rebecca
AU - Barboni, Piero
AU - Cascavilla, Maria L.
AU - Maresca, Alessandra
AU - Capristo, Mariantonietta
AU - Ardissone, Anna
AU - Pareyson, Davide
AU - Cammarata, Gabriella
AU - Melzi, Lisa
AU - Zeviani, Massimo
AU - Peverelli, Lorenzo
AU - Lamperti, Costanza
AU - Marzoli, Stefania B.
AU - Fang, Mingyan
AU - Synofzik, Matthis
AU - Ghezzi, Daniele
AU - Carelli, Valerio
AU - Taroni, Franco
TI - ATPase Domain AFG3L2 Mutations Alter OPA1 Processing and Cause Optic Neuropathy
JO - Annals of neurology
VL - 88
IS - 1
SN - 1531-8249
CY - Hoboken, NJ
PB - Wiley-Blackwell
M1 - DZNE-2020-01239
SP - 18 - 32
PY - 2020
AB - ObjectiveDominant optic atrophy (DOA) is the most common inherited optic neuropathy, with a prevalence of 1:12,000 to 1:25,000. OPA1 mutations are found in 70
KW - ATP-Dependent Proteases: genetics
KW - ATPases Associated with Diverse Cellular Activities: genetics
KW - Adolescent
KW - Adult
KW - Aged
KW - Child
KW - Female
KW - GTP Phosphohydrolases: genetics
KW - Genetic Testing
KW - High-Throughput Nucleotide Sequencing
KW - Humans
KW - Male
KW - Middle Aged
KW - Mutation
KW - Optic Atrophy: genetics
KW - Optic Nerve Diseases: genetics
KW - Pedigree
KW - Exome Sequencing
KW - Young Adult
LB - PUB:(DE-HGF)16
C2 - pmc:PMC7383914
C6 - pmid:32219868
DO - DOI:10.1002/ana.25723
UR - https://pub.dzne.de/record/151660
ER -