% IMPORTANT: The following is UTF-8 encoded. This means that in the presence
% of non-ASCII characters, it will not work with BibTeX 0.99 or older.
% Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or
% “biber”.
@ARTICLE{Briel:155769,
author = {Briel, Nils and Pratsch, Katrin and Roeber, Sigrun and
Arzberger, Thomas and Herms, Jochen},
title = {{C}ontribution of the astrocytic tau pathology to synapse
loss in progressive supranuclear palsy and corticobasal
degeneration.},
journal = {Brain pathology},
volume = {31},
number = {4},
issn = {1750-3639},
address = {Oxford},
publisher = {Wiley-Blackwell},
reportid = {DZNE-2021-00937},
pages = {e12914},
year = {2021},
abstract = {Primary 4-repeat tauopathies with frontotemporal lobar
degeneration (FTLD) like Progressive Supranuclear Palsy
(PSP) or Corticobasal Degeneration (CBD) show diverse
cellular pathology in various brain regions. Besides shared
characteristics of neuronal and oligodendroglial cytoplasmic
inclusions of accumulated hyperphosphorylated tau protein
(pTau), astrocytes in PSP and CBD contain pathognomonic pTau
aggregates - hence, lending the designation tufted
astrocytes (TA) or astrocytic plaques (AP), respectively.
pTau toxicity is most commonly assigned to neurons, whereas
the implications of astrocytic pTau for maintaining
neurotransmission within the tripartite synapse of human
brains is not well understood. We performed
immunofluorescent synapse labeling and automated puncta
quantification in the medial frontal gyrus (MFG) and
striatal regions from PSP and CBD postmortem samples to
capture morphometric synaptic alterations. This approach
indicated general synaptic losses of both, excitatory and
inhibitory bipartite synapses in the frontal cortex of PSP
cases, whereas in CBD lower synapse densities were only
related to astrocytic plaques. In contrast to tufted
astrocytes in PSP, affected astrocytes in CBD could not
preserve synaptic integrity within their spatial domains,
when compared to non-affected internal astrocytes or
astrocytes in healthy controls. These findings suggest a
pTau pathology-associated role of astrocytes in maintaining
connections within neuronal circuits, considered as the
microscopic substrate of cognitive dysfunction in CBD. By
contrasting astrocytic-synaptic associations in both
diseases, we hereby highlight astrocytic pTau as an
important subject of prospective research and as a potential
cellular target for therapeutic approaches in the primary
tauopathies PSP and CBD.},
keywords = {Aged / Aged, 80 and over / Astrocytes: pathology / Brain:
pathology / Corticobasal Degeneration: pathology / Female /
Frontotemporal Lobar Degeneration: pathology / Humans /
Inclusion Bodies: pathology / Male / Middle Aged / Neurons:
pathology / Supranuclear Palsy, Progressive: metabolism /
Supranuclear Palsy, Progressive: pathology / Tauopathies:
pathology / tau Proteins: metabolism / astrocytic plaques
(Other) / corticobasal degeneration (Other) / progressive
supranuclear palsy (Other) / synapse loss (Other) /
tauopathy (Other) / tufted astrocytes (Other)},
cin = {AG Herms / Neuropathology / Brainbank},
ddc = {610},
cid = {I:(DE-2719)1110001 / I:(DE-2719)1140013},
pnm = {352 - Disease Mechanisms (POF4-352)},
pid = {G:(DE-HGF)POF4-352},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:33089580},
pmc = {pmc:PMC8412068},
doi = {10.1111/bpa.12914},
url = {https://pub.dzne.de/record/155769},
}