000157728 001__ 157728 000157728 005__ 20240123093027.0 000157728 0247_ $$2doi$$a10.1016/j.jneumeth.2021.109141 000157728 0247_ $$2pmid$$apmid:33753124 000157728 0247_ $$2ISSN$$a0165-0270 000157728 0247_ $$2ISSN$$a1872-678X 000157728 0247_ $$2altmetric$$aaltmetric:102532506 000157728 037__ $$aDZNE-2021-01185 000157728 041__ $$aEnglish 000157728 082__ $$a610 000157728 1001_ $$aWaldt, Natalie$$b0 000157728 245__ $$aCrispr/Cas-based modeling of NF2 loss in meningioma cells. 000157728 260__ $$aAmsterdam [u.a.]$$bElsevier Science$$c2021 000157728 3367_ $$2DRIVER$$aarticle 000157728 3367_ $$2DataCite$$aOutput Types/Journal article 000157728 3367_ $$0PUB:(DE-HGF)16$$2PUB:(DE-HGF)$$aJournal Article$$bjournal$$mjournal$$s1705998584_18611 000157728 3367_ $$2BibTeX$$aARTICLE 000157728 3367_ $$2ORCID$$aJOURNAL_ARTICLE 000157728 3367_ $$00$$2EndNote$$aJournal Article 000157728 520__ $$aAlterations of the neurofibromatosis type 2 gene (NF2) occur in more than fifty percent of sporadic meningiomas. Meningiomas develop frequently in the setting of the hereditary tumor syndrome NF2. Investigation of potential drug-based treatment options has been limited by the lack of appropriate in vitro and in vivo models.Using Crispr/Cas gene editing, of the malignant meningioma cell line IOMM-Lee, we generated a pair of cell clones characterized by either stable knockout of NF2 and loss of the protein product merlin or retained merlin protein (transfected control without gRNA).IOMM-Lee cells lacking NF2 showed reduced apoptosis and formed bigger colonies compared to control IOMM-Lee cells. Treatment of non-transfected IOMM-Lee cells with the focal adhesion kinase (FAK) inhibitor GSK2256098 resulted in reduced colony sizes. Orthotopic mouse xenografts showed the formation of convexity tumors typical for meningiomas with NF2-depleted and control cells.No orthotopic meningioma models with genetically-engineered cell pairs are available so far.Our model based on Crispr/Cas-based gene editing provides paired meningioma cells suitable to study functional consequences and therapeutic accessibility of NF2/merlin loss. 000157728 536__ $$0G:(DE-HGF)POF4-351$$a351 - Brain Function (POF4-351)$$cPOF4-351$$fPOF IV$$x0 000157728 588__ $$aDataset connected to CrossRef, PubMed, , Journals: pub.dzne.de 000157728 650_7 $$2Other$$aCrispr/Cas 000157728 650_7 $$2Other$$aMeningioma 000157728 650_7 $$2Other$$aNeurofibromatosis type 2 (NF2) 000157728 650_7 $$2NLM Chemicals$$aNeurofibromin 2 000157728 650_2 $$2MeSH$$aAnimals 000157728 650_2 $$2MeSH$$aCell Line, Tumor 000157728 650_2 $$2MeSH$$aClustered Regularly Interspaced Short Palindromic Repeats: genetics 000157728 650_2 $$2MeSH$$aMeningeal Neoplasms: genetics 000157728 650_2 $$2MeSH$$aMeningioma: genetics 000157728 650_2 $$2MeSH$$aMice 000157728 650_2 $$2MeSH$$aNeurofibromin 2: genetics 000157728 650_2 $$2MeSH$$aNeurofibromin 2: metabolism 000157728 7001_ $$aKesseler, Christoph$$b1 000157728 7001_ $$aFala, Paula$$b2 000157728 7001_ $$aJohn, Peter$$b3 000157728 7001_ $$aKirches, Elmar$$b4 000157728 7001_ $$0P:(DE-2719)2810456$$aAngenstein, Frank$$b5$$udzne 000157728 7001_ $$aMawrin, Christian$$b6 000157728 773__ $$0PERI:(DE-600)1500499-5$$a10.1016/j.jneumeth.2021.109141$$gVol. 356, p. 109141 -$$p109141$$tJournal of neuroscience methods$$v356$$x0165-0270$$y2021 000157728 8564_ $$uhttps://pub.dzne.de/record/157728/files/DZNE-2021-01185_Restricted.pdf 000157728 8564_ $$uhttps://pub.dzne.de/record/157728/files/DZNE-2021-01185_Restricted.pdf?subformat=pdfa$$xpdfa 000157728 909CO $$ooai:pub.dzne.de:157728$$pVDB 000157728 9101_ $$0I:(DE-588)1065079516$$6P:(DE-2719)2810456$$aDeutsches Zentrum für Neurodegenerative Erkrankungen$$b5$$kDZNE 000157728 9131_ $$0G:(DE-HGF)POF4-351$$1G:(DE-HGF)POF4-350$$2G:(DE-HGF)POF4-300$$3G:(DE-HGF)POF4$$4G:(DE-HGF)POF$$aDE-HGF$$bGesundheit$$lNeurodegenerative Diseases$$vBrain Function$$x0 000157728 9141_ $$y2021 000157728 915__ $$0StatID:(DE-HGF)0160$$2StatID$$aDBCoverage$$bEssential Science Indicators$$d2021-01-27 000157728 915__ $$0StatID:(DE-HGF)1190$$2StatID$$aDBCoverage$$bBiological Abstracts$$d2021-01-27 000157728 915__ $$0StatID:(DE-HGF)0113$$2StatID$$aWoS$$bScience Citation Index Expanded$$d2021-01-27 000157728 915__ $$0StatID:(DE-HGF)0420$$2StatID$$aNationallizenz$$d2022-11-12$$wger 000157728 915__ $$0StatID:(DE-HGF)0300$$2StatID$$aDBCoverage$$bMedline$$d2022-11-12 000157728 915__ $$0StatID:(DE-HGF)0199$$2StatID$$aDBCoverage$$bClarivate Analytics Master Journal List$$d2022-11-12 000157728 915__ $$0StatID:(DE-HGF)0150$$2StatID$$aDBCoverage$$bWeb of Science Core Collection$$d2022-11-12 000157728 915__ $$0StatID:(DE-HGF)1050$$2StatID$$aDBCoverage$$bBIOSIS Previews$$d2022-11-12 000157728 915__ $$0StatID:(DE-HGF)1030$$2StatID$$aDBCoverage$$bCurrent Contents - Life Sciences$$d2022-11-12 000157728 915__ $$0StatID:(DE-HGF)0100$$2StatID$$aJCR$$bJ NEUROSCI METH : 2021$$d2022-11-12 000157728 915__ $$0StatID:(DE-HGF)0200$$2StatID$$aDBCoverage$$bSCOPUS$$d2022-11-12 000157728 915__ $$0StatID:(DE-HGF)0600$$2StatID$$aDBCoverage$$bEbsco Academic Search$$d2022-11-12 000157728 915__ $$0StatID:(DE-HGF)0030$$2StatID$$aPeer Review$$bASC$$d2022-11-12 000157728 915__ $$0StatID:(DE-HGF)9900$$2StatID$$aIF < 5$$d2022-11-12 000157728 9201_ $$0I:(DE-2719)1310004$$kAG Angenstein$$lFunctional Neuroimaging$$x0 000157728 980__ $$ajournal 000157728 980__ $$aVDB 000157728 980__ $$aI:(DE-2719)1310004 000157728 980__ $$aUNRESTRICTED