% IMPORTANT: The following is UTF-8 encoded. This means that in the presence % of non-ASCII characters, it will not work with BibTeX 0.99 or older. % Instead, you should use an up-to-date BibTeX implementation like “bibtex8” or % “biber”. @ARTICLE{Ramachandran:259703, author = {Ramachandran, Swetha and Grozdanov, Veselin and Leins, Bianca and Kandler, Katharina and Witzel, Simon and Mulaw, Medhanie and Ludolph, Albert C. and Weishaupt, Jochen H. and Danzer, Karin M.}, title = {{L}ow {T}-cell reactivity to {TDP}-43 peptides in {ALS}}, journal = {Frontiers in immunology}, volume = {14}, issn = {1664-3224}, address = {Lausanne}, publisher = {Frontiers Media}, reportid = {DZNE-2023-00775}, pages = {1193507}, year = {2023}, abstract = {Dysregulation of the immune system in amyotrophic lateral sclerosis (ALS) includes changes in T-cells composition and infiltration of T cells in the brain and spinal cord. Recent studies have shown that cytotoxic T cells can directly induce motor neuron death in a mouse model of ALS and that T cells from ALS patients are cytotoxic to iPSC-derived motor neurons from ALS patients. Furthermore, a clonal expansion to unknown epitope(s) was recently found in familial ALS and increased peripheral and intrathecal activation of cytotoxic CD8+ T cells in sporadic ALS.Here, we show an increased activation of peripheral T cells from patients with sporadic ALS by IL-2 treatment, suggesting an increase of antigen-experienced T cells in ALS blood. However, a putative antigen for T-cell activation in ALS has not yet been identified. Therefore, we investigated if peptides derived from TDP-43, a key protein in ALS pathogenesis, can act as epitopes for antigen-mediated activation of human T cells by ELISPOT and flow cytometry. We found that TDP-43 peptides induced only a weak MHCI or MHCII-restricted activation of both naïve and antigen-experienced T cells from healthy controls and ALS patients. Interestingly, we found less activation in T cells from ALS patients to TDP-43 and control stimuli. Furthermore, we found no change in the levels of naturally occurring auto-antibodies against full-length TDP-43 in ALS.Our data suggests a general increase in antigen-experienced T cells in ALS blood, measured by in-vitro culture with IL-2 for 14 days. Furthermore, it suggests that TDP-43 is a weak autoantigen.}, keywords = {Humans / Amyotrophic Lateral Sclerosis: metabolism / CD8-Positive T-Lymphocytes: metabolism / DNA-Binding Proteins: metabolism / Interleukin-2 / DNA-Binding Proteins (NLM Chemicals) / T cells (Other) / TDP-43 (Other) / amyotrophic lateral sclerosis (Other) / autoantibody (Other) / autoantigen (Other) / Interleukin-2 (NLM Chemicals) / TARDBP protein, human (NLM Chemicals)}, cin = {AG Danzer / Clinical Study Center Ulm}, ddc = {610}, cid = {I:(DE-2719)5000072 / I:(DE-2719)5000077}, pnm = {352 - Disease Mechanisms (POF4-352) / 353 - Clinical and Health Care Research (POF4-353)}, pid = {G:(DE-HGF)POF4-352 / G:(DE-HGF)POF4-353}, typ = {PUB:(DE-HGF)16}, pmc = {pmc:PMC10401033}, pubmed = {pmid:37545536}, doi = {10.3389/fimmu.2023.1193507}, url = {https://pub.dzne.de/record/259703}, }