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@ARTICLE{Jackson:269354,
author = {Jackson, Joshua and Hoffmann, Christian and Scifo, Enzo and
Wang, Han and Wischhof, Lena and Piazzesi, Antonia and
Mondal, Mrityunjoy and Shields, Hanna and Zhou, Xuesi and
Mondin, Magali and Ryan, Eanna B and Döring, Hermann and
Prehn, Jochen H M and Rottner, Klemens and Giannone, Gregory
and Nicotera, Pierluigi and Ehninger, Dan and Milovanovic,
Dragomir and Bano, Daniele},
title = {{A}ctin-nucleation promoting factor {N}-{WASP} influences
alpha-synuclein condensates and pathology.},
journal = {Cell death $\&$ disease},
volume = {15},
number = {4},
issn = {2041-4889},
address = {London [u.a.]},
publisher = {Nature Publishing Group},
reportid = {DZNE-2024-00522},
pages = {304},
year = {2024},
abstract = {Abnormal intraneuronal accumulation of soluble and
insoluble α-synuclein (α-Syn) is one of the main
pathological hallmarks of synucleinopathies, such as
Parkinson's disease (PD). It has been well documented that
the reversible liquid-liquid phase separation of α-Syn can
modulate synaptic vesicle condensates at the presynaptic
terminals. However, α-Syn can also form liquid-like
droplets that may convert into amyloid-enriched hydrogels or
fibrillar polymorphs under stressful conditions. To advance
our understanding on the mechanisms underlying α-Syn phase
transition, we employed a series of unbiased proteomic
analyses and found that actin and actin regulators are part
of the α-Syn interactome. We focused on Neural
Wiskott-Aldrich syndrome protein (N-WASP) because of its
association with a rare early-onset familial form of PD. In
cultured cells, we demonstrate that N-WASP undergoes phase
separation and can be recruited to synapsin 1 liquid-like
droplets, whereas it is excluded from α-Syn/synapsin 1
condensates. Consistently, we provide evidence that
wsp-1/WASL loss of function alters the number and dynamics
of α-Syn inclusions in the nematode Caenorhabditis elegans.
Together, our findings indicate that N-WASP expression may
create permissive conditions that promote α-Syn condensates
and their potentially deleterious conversion into toxic
species.},
keywords = {alpha-Synuclein: metabolism / Animals / Humans /
Caenorhabditis elegans: metabolism / Wiskott-Aldrich
Syndrome Protein, Neuronal: metabolism / Actins: metabolism
/ Parkinson Disease: metabolism / Parkinson Disease:
pathology / Synapsins: metabolism / Caenorhabditis elegans
Proteins: metabolism / alpha-Synuclein (NLM Chemicals) /
Wiskott-Aldrich Syndrome Protein, Neuronal (NLM Chemicals) /
Actins (NLM Chemicals) / WASL protein, human (NLM Chemicals)
/ Synapsins (NLM Chemicals) / Caenorhabditis elegans
Proteins (NLM Chemicals)},
cin = {AG Bano / AG Milovanovic / AG Ehninger},
ddc = {570},
cid = {I:(DE-2719)1013003 / I:(DE-2719)1813002 /
I:(DE-2719)1013005},
pnm = {351 - Brain Function (POF4-351) / 352 - Disease Mechanisms
(POF4-352)},
pid = {G:(DE-HGF)POF4-351 / G:(DE-HGF)POF4-352},
typ = {PUB:(DE-HGF)16},
pmc = {pmc:PMC11063037},
pubmed = {pmid:38693139},
doi = {10.1038/s41419-024-06686-7},
url = {https://pub.dzne.de/record/269354},
}