000272852 001__ 272852 000272852 005__ 20241029085454.0 000272852 0247_ $$2doi$$a10.1002/mds.29879 000272852 0247_ $$2pmid$$apmid:38847384 000272852 0247_ $$2ISSN$$a0885-3185 000272852 0247_ $$2ISSN$$a1531-8257 000272852 0247_ $$2altmetric$$aaltmetric:164390137 000272852 037__ $$aDZNE-2024-01270 000272852 041__ $$aEnglish 000272852 082__ $$a610 000272852 1001_ $$0P:(DE-2719)9003066$$aJensen, Ida Marie Louise$$b0$$udzne 000272852 245__ $$aImpact of Magnetic Resonance Imaging Markers on the Diagnostic Performance of the International Parkinson and Movement Disorder Society Multiple System Atrophy Criteria. 000272852 260__ $$aNew York, NY$$bWiley$$c2024 000272852 3367_ $$2DRIVER$$aarticle 000272852 3367_ $$2DataCite$$aOutput Types/Journal article 000272852 3367_ $$0PUB:(DE-HGF)16$$2PUB:(DE-HGF)$$aJournal Article$$bjournal$$mjournal$$s1729780484_26451 000272852 3367_ $$2BibTeX$$aARTICLE 000272852 3367_ $$2ORCID$$aJOURNAL_ARTICLE 000272852 3367_ $$00$$2EndNote$$aJournal Article 000272852 520__ $$aMultiple system atrophy is a neurodegenerative disease with α-synuclein aggregation in glial cytoplasmic inclusions, leading to dysautonomia, parkinsonism, and cerebellar ataxia.The aim of this study was to validate the accuracy of the International Parkinson and Movement Disorder Society Multiple System Atrophy clinical diagnostic criteria, particularly considering the impact of the newly introduced brain magnetic resonance imaging (MRI) markers.Diagnostic accuracy of the clinical diagnostic criteria for multiple system atrophy was estimated retrospectively in autopsy-confirmed patients with multiple system atrophy, Parkinson's disease, progressive supranuclear palsy, and corticobasal degeneration.We identified a total of 240 patients. Sensitivity of the clinically probable criteria was moderate at symptom onset but improved with disease duration (year 1: 9%, year 3: 39%, final ante mortem record: 77%), whereas their specificity remained consistently high (99%-100% throughout). Sensitivity of the clinically established criteria was low during the first 3 years (1%-9%), with mild improvement at the final ante mortem record (22%), whereas specificity remained high (99%-100% throughout). When MRI features were excluded from the clinically established criteria, their sensitivity increased considerably (year 1: 3%, year 3: 22%, final ante mortem record: 48%), and their specificity was not compromised (99%-100% throughout).The International Parkinson and Movement Disorder Society multiple system atrophy diagnostic criteria showed consistently high specificity and low to moderate sensitivity throughout the disease course. The MRI markers for the clinically established criteria reduced their sensitivity without improving specificity. Combining clinically probable and clinically established criteria, but disregarding MRI features, yielded the best sensitivity with excellent specificity and may be most appropriate to select patients for therapeutic trials. © 2024 The Author(s). Movement Disorders published by Wiley Periodicals LLC on behalf of International Parkinson and Movement Disorder Society. 000272852 536__ $$0G:(DE-HGF)POF4-353$$a353 - Clinical and Health Care Research (POF4-353)$$cPOF4-353$$fPOF IV$$x0 000272852 536__ $$0G:(DE-HGF)POF4-352$$a352 - Disease Mechanisms (POF4-352)$$cPOF4-352$$fPOF IV$$x1 000272852 588__ $$aDataset connected to CrossRef, PubMed, , Journals: pub.dzne.de 000272852 650_7 $$2Other$$aMRI 000272852 650_7 $$2Other$$aautopsy‐confirmed 000272852 650_7 $$2Other$$abrain magnetic resonance imaging 000272852 650_7 $$2Other$$amultiple system atrophy 000272852 650_2 $$2MeSH$$aHumans 000272852 650_2 $$2MeSH$$aMultiple System Atrophy: diagnostic imaging 000272852 650_2 $$2MeSH$$aMultiple System Atrophy: diagnosis 000272852 650_2 $$2MeSH$$aFemale 000272852 650_2 $$2MeSH$$aMale 000272852 650_2 $$2MeSH$$aAged 000272852 650_2 $$2MeSH$$aMiddle Aged 000272852 650_2 $$2MeSH$$aParkinson Disease: diagnostic imaging 000272852 650_2 $$2MeSH$$aParkinson Disease: diagnosis 000272852 650_2 $$2MeSH$$aMagnetic Resonance Imaging: standards 000272852 650_2 $$2MeSH$$aMagnetic Resonance Imaging: methods 000272852 650_2 $$2MeSH$$aRetrospective Studies 000272852 650_2 $$2MeSH$$aSupranuclear Palsy, Progressive: diagnostic imaging 000272852 650_2 $$2MeSH$$aSensitivity and Specificity 000272852 650_2 $$2MeSH$$aBrain: diagnostic imaging 000272852 650_2 $$2MeSH$$aBrain: pathology 000272852 650_2 $$2MeSH$$aAged, 80 and over 000272852 7001_ $$aHeine, Johanne$$b1 000272852 7001_ $$aRuf, Viktoria C$$b2 000272852 7001_ $$aCompta, Yaroslau$$b3 000272852 7001_ $$aPorcel, Laura Molina$$b4 000272852 7001_ $$aTroakes, Claire$$b5 000272852 7001_ $$aVamanu, Albert$$b6 000272852 7001_ $$aDownes, Sophia$$b7 000272852 7001_ $$aIrwin, David$$b8 000272852 7001_ $$00000-0003-2554-5181$$aCohen, Jesse$$b9 000272852 7001_ $$aLee, Edward B$$b10 000272852 7001_ $$aNilsson, Christer$$b11 000272852 7001_ $$aEnglund, Elisabet$$b12 000272852 7001_ $$0P:(DE-2719)9002938$$aNemati, Mojtaba$$b13$$udzne 000272852 7001_ $$0P:(DE-2719)9001160$$aKatzdobler, Sabrina$$b14$$udzne 000272852 7001_ $$0P:(DE-2719)2811659$$aLevin, Johannes$$b15$$udzne 000272852 7001_ $$00000-0002-6427-7485$$aPantelyat, Alex$$b16 000272852 7001_ $$aSeemiller, Joseph$$b17 000272852 7001_ $$aBerger, Stephen$$b18 000272852 7001_ $$avan Swieten, John$$b19 000272852 7001_ $$aDopper, Elise$$b20 000272852 7001_ $$aRozenmuller, Annemieke$$b21 000272852 7001_ $$aKovacs, Gabor G$$b22 000272852 7001_ $$00000-0003-2167-5667$$aBendahan, Nathaniel$$b23 000272852 7001_ $$aLang, Anthony E$$b24 000272852 7001_ $$0P:(DE-2719)2810441$$aHerms, Jochen$$b25$$udzne 000272852 7001_ $$0P:(DE-2719)2811373$$aHöglinger, Günter$$b26 000272852 7001_ $$0P:(DE-2719)9003372$$aHopfner, Franziska$$b27$$udzne 000272852 773__ $$0PERI:(DE-600)2041249-6$$a10.1002/mds.29879$$gVol. 39, no. 9, p. 1514 - 1522$$n9$$p1514 - 1522$$tMovement disorders$$v39$$x0885-3185$$y2024 000272852 8564_ $$uhttps://pub.dzne.de/record/272852/files/DZNE-2024-01270.pdf$$yOpenAccess 000272852 8564_ $$uhttps://pub.dzne.de/record/272852/files/DZNE-2024-01270.pdf?subformat=pdfa$$xpdfa$$yOpenAccess 000272852 909CO $$ooai:pub.dzne.de:272852$$pdnbdelivery$$pdriver$$pVDB$$popen_access$$popenaire 000272852 9101_ $$0I:(DE-HGF)0$$6P:(DE-2719)9003066$$aExternal Institute$$b0$$kExtern 000272852 9101_ $$0I:(DE-HGF)0$$6P:(DE-2719)9002938$$aExternal Institute$$b13$$kExtern 000272852 9101_ $$0I:(DE-HGF)0$$6P:(DE-2719)9001160$$aExternal Institute$$b14$$kExtern 000272852 9101_ $$0I:(DE-588)1065079516$$6P:(DE-2719)2811659$$aDeutsches Zentrum für Neurodegenerative Erkrankungen$$b15$$kDZNE 000272852 9101_ $$0I:(DE-588)1065079516$$6P:(DE-2719)2810441$$aDeutsches Zentrum für Neurodegenerative Erkrankungen$$b25$$kDZNE 000272852 9101_ $$0I:(DE-588)1065079516$$6P:(DE-2719)2811373$$aDeutsches Zentrum für Neurodegenerative Erkrankungen$$b26$$kDZNE 000272852 9101_ $$0I:(DE-HGF)0$$6P:(DE-2719)9003372$$aExternal Institute$$b27$$kExtern 000272852 9131_ $$0G:(DE-HGF)POF4-353$$1G:(DE-HGF)POF4-350$$2G:(DE-HGF)POF4-300$$3G:(DE-HGF)POF4$$4G:(DE-HGF)POF$$aDE-HGF$$bGesundheit$$lNeurodegenerative Diseases$$vClinical and Health Care Research$$x0 000272852 9131_ $$0G:(DE-HGF)POF4-352$$1G:(DE-HGF)POF4-350$$2G:(DE-HGF)POF4-300$$3G:(DE-HGF)POF4$$4G:(DE-HGF)POF$$aDE-HGF$$bGesundheit$$lNeurodegenerative Diseases$$vDisease Mechanisms$$x1 000272852 9141_ $$y2024 000272852 915__ $$0StatID:(DE-HGF)0200$$2StatID$$aDBCoverage$$bSCOPUS$$d2023-10-24 000272852 915__ $$0StatID:(DE-HGF)0160$$2StatID$$aDBCoverage$$bEssential Science Indicators$$d2023-10-24 000272852 915__ $$0StatID:(DE-HGF)1030$$2StatID$$aDBCoverage$$bCurrent Contents - Life Sciences$$d2023-10-24 000272852 915__ $$0StatID:(DE-HGF)0600$$2StatID$$aDBCoverage$$bEbsco Academic Search$$d2023-10-24 000272852 915__ $$0LIC:(DE-HGF)CCBYNCND4$$2HGFVOC$$aCreative Commons Attribution-NonCommercial-NoDerivs CC BY-NC-ND 4.0 000272852 915__ $$0StatID:(DE-HGF)0100$$2StatID$$aJCR$$bMOVEMENT DISORD : 2022$$d2023-10-24 000272852 915__ $$0StatID:(DE-HGF)3001$$2StatID$$aDEAL Wiley$$d2023-10-24$$wger 000272852 915__ $$0StatID:(DE-HGF)0113$$2StatID$$aWoS$$bScience Citation Index Expanded$$d2023-10-24 000272852 915__ $$0StatID:(DE-HGF)0150$$2StatID$$aDBCoverage$$bWeb of Science Core Collection$$d2023-10-24 000272852 915__ $$0StatID:(DE-HGF)0510$$2StatID$$aOpenAccess 000272852 915__ $$0StatID:(DE-HGF)0030$$2StatID$$aPeer Review$$bASC$$d2023-10-24 000272852 915__ $$0StatID:(DE-HGF)9905$$2StatID$$aIF >= 5$$bMOVEMENT DISORD : 2022$$d2023-10-24 000272852 915__ $$0StatID:(DE-HGF)0300$$2StatID$$aDBCoverage$$bMedline$$d2023-10-24 000272852 915__ $$0StatID:(DE-HGF)1110$$2StatID$$aDBCoverage$$bCurrent Contents - Clinical Medicine$$d2023-10-24 000272852 915__ $$0StatID:(DE-HGF)0420$$2StatID$$aNationallizenz$$d2023-10-24$$wger 000272852 915__ $$0StatID:(DE-HGF)0199$$2StatID$$aDBCoverage$$bClarivate Analytics Master Journal List$$d2023-10-24 000272852 9201_ $$0I:(DE-2719)1110002$$kAG Höglinger$$lTranslational Neurodegeneration$$x0 000272852 9201_ $$0I:(DE-2719)1110001$$kAG Herms$$lTranslational Brain Research$$x1 000272852 9201_ $$0I:(DE-2719)1111015$$kClinical Research (Munich)$$lClinical Research (Munich)$$x2 000272852 980__ $$ajournal 000272852 980__ $$aVDB 000272852 980__ $$aUNRESTRICTED 000272852 980__ $$aI:(DE-2719)1110002 000272852 980__ $$aI:(DE-2719)1110001 000272852 980__ $$aI:(DE-2719)1111015 000272852 9801_ $$aFullTexts