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@ARTICLE{vonderGablentz:273926,
author = {von der Gablentz, Janina and Overbeeke, Nina and Timmann,
Dagmar and Ganos, Christos and Synofzik, Matthis and
Brüggemann, Norbert and Helmchen, Christoph and Sprenger,
Andreas},
title = {{P}ostural control in episodic ataxia type 2: no evidence
for increased vestibular excitability},
journal = {European journal of neurology},
volume = {32},
number = {1},
issn = {1351-5101},
address = {Oxford [u.a.]},
publisher = {Wiley-Blackwell},
reportid = {DZNE-2024-01400},
pages = {e16520},
year = {2025},
abstract = {Patients with episodic ataxia type 2 (EA2) suffer from
recurrent paroxysmal episodes of vertigo and oscillopsia.
Pathophysiologically, altered neuronal excitability has been
suspected. Vestibular excitability in 22 EA2 patients and 22
age-matched healthy participants was compared.Galvanic
vestibular stimulation (GVS) was used to assess vestibular
excitability by vestibular motion perception thresholds and
mean postural sway velocity during various visual and
proprioceptive conditions in the two groups. Control stimuli
using sham and no GVS were established to identify the
specificity of GVS-induced postural sway.In the baseline
condition, EA2 patients showed larger postural instability.
However, motion perception thresholds and the increase in
mean postural sway velocity during vestibular stimulation
(stimulation ratio) did not differ between groups. Postural
sway during suprathreshold GVS increased with the vestibular
motion perception threshold in EA2 patients, in contrast to
healthy participants.The larger postural unsteadiness of EA2
patients probably reflects their progressive cerebellar
degeneration. It is not related to abnormal visual
(Romberg's ratio) or proprioceptive control of stance.
Postural unsteadiness during vestibular stimulation does not
indicate altered vestibular excitability in EA2 patients.
However, vestibular stimulation increasingly destabilized
postural control of EA2 patients with higher motion
perception thresholds when proprioceptive information was
diminished. This conclusion, however, is restricted to the
postural control of EA2 patients in the interval between the
vestibulo-cerebellar episodes.},
keywords = {Humans / Female / Male / Postural Balance: physiology /
Middle Aged / Adult / Ataxia: physiopathology / Vestibule,
Labyrinth: physiopathology / Vestibule, Labyrinth:
physiology / Aged / Motion Perception: physiology / Electric
Stimulation / Nystagmus, Pathologic},
cin = {AG Gasser},
ddc = {610},
cid = {I:(DE-2719)1210000},
pnm = {353 - Clinical and Health Care Research (POF4-353)},
pid = {G:(DE-HGF)POF4-353},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:39463030},
pmc = {pmc:PMC11622321},
doi = {10.1111/ene.16520},
url = {https://pub.dzne.de/record/273926},
}