TY - JOUR AU - Klose, Veronika AU - Jesse, Sarah AU - Lewerenz, Jan AU - Kassubek, Jan AU - Dorst, Johannes AU - Rosenbohm, Angela AU - Nagel, Gabriele AU - Wernecke, Deborah AU - Roselli, Francesco AU - Tumani, Hayrettin AU - Ludolph, Albert C TI - Blood-CSF barrier integrity in amyotrophic lateral sclerosis. JO - Brain VL - 147 IS - 12 SN - 0006-8950 CY - Oxford PB - Oxford Univ. Press M1 - DZNE-2024-01414 SP - 4254 - 4264 PY - 2024 AB - The integrity of the blood-CSF barrier plays a major role in inflammation, but also in shielding the CNS from external and systemic-potentially toxic-factors. Here we report results of measurements of the albumin quotient-which is thought to mirror the integrity of the blood-CSF barrier-in 1059 patients with amyotrophic lateral sclerosis. The results were compared with groups of patients suffering from Alzheimer's disease, facial palsy and tension headache. The albumin quotient, an accepted measure of the blood-CSF barrier integrity, was not significantly different from control populations. In addition, we found that the albumin quotient correlated with survival of the patients; this effect was mainly driven by male patients and influenced by age, body mass index and diabetes mellitus. We conclude that the blood-CSF barrier is intact in this large cohort of patients with amyotrophic lateral sclerosis and that the albumin quotient correlates with survival. Whether this is important for the pathogenesis of the disease, requires mechanistic studies. KW - Humans KW - Amyotrophic Lateral Sclerosis KW - Male KW - Female KW - Middle Aged KW - Aged KW - Blood-Brain Barrier: metabolism KW - Adult KW - Albumins: metabolism KW - Aged, 80 and over KW - Cohort Studies KW - albumin quotient (Other) KW - amyotrophic lateral sclerosis (Other) KW - blood-CSF barrier (Other) KW - cerebrospinal fluid (Other) KW - survival (Other) KW - Albumins (NLM Chemicals) LB - PUB:(DE-HGF)16 C6 - pmid:38743595 DO - DOI:10.1093/brain/awae144 UR - https://pub.dzne.de/record/273940 ER -