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@ARTICLE{Soto:276802,
author = {Soto, Claudio and Mollenhauer, Brit and Hansson, Oskar and
Kang, Un Jung and Alcalay, Roy N and Standaert, David and
Trenkwalder, Claudia and Marek, Kenneth and Galasko, Douglas
and Poston, Kathleen},
title = {{T}oward a biological definition of neuronal and glial
synucleinopathies.},
journal = {Nature medicine},
volume = {31},
number = {2},
issn = {1078-8956},
address = {[New York, NY]},
publisher = {Springer Nature},
reportid = {DZNE-2025-00327},
pages = {396 - 408},
year = {2025},
abstract = {Cerebral accumulation of alpha-synuclein (αSyn) aggregates
is the hallmark event in a group of neurodegenerative
diseases-collectively called synucleinopathies-which include
Parkinson's disease, dementia with Lewy bodies and multiple
system atrophy. Currently, these are diagnosed by their
clinical symptoms and definitively confirmed postmortem by
the presence of αSyn deposits in the brain. Here, we
summarize the drawbacks of the current clinical definition
of synucleinopathies and outline the rationale for moving
toward an earlier, biology-anchored definition of these
disorders, with or without the presence of clinical
symptoms. We underscore the utility of the αSyn seed
amplification assay to detect aggregated αSyn in living
patients and to differentiate between neuronal or glial
αSyn pathology. We anticipate that a biological definition
of synucleinopathies, if well-integrated with the current
clinical classifications, will enable further understanding
of the disease pathogenesis and contribute to the
development of effective, disease-modifying therapies.},
subtyp = {Review Article},
keywords = {Humans / Neuroglia: pathology / Neuroglia: metabolism /
alpha-Synuclein: metabolism / alpha-Synuclein: genetics /
Synucleinopathies: pathology / Synucleinopathies: metabolism
/ Neurons: pathology / Neurons: metabolism / Parkinson
Disease: pathology / Parkinson Disease: genetics / Parkinson
Disease: metabolism / Brain: pathology / Brain: metabolism /
Multiple System Atrophy: pathology / Multiple System
Atrophy: metabolism / Multiple System Atrophy: genetics /
Lewy Body Disease: pathology / Lewy Body Disease: metabolism
/ Lewy Body Disease: genetics / alpha-Synuclein (NLM
Chemicals)},
cin = {AG Fischer},
ddc = {610},
cid = {I:(DE-2719)1410002},
pnm = {352 - Disease Mechanisms (POF4-352)},
pid = {G:(DE-HGF)POF4-352},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:39885358},
doi = {10.1038/s41591-024-03469-7},
url = {https://pub.dzne.de/record/276802},
}