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@ARTICLE{Cinar:281436,
author = {Cinar, Elif and Yalcin-Cakmakli, Gül and Akyel, Hilal and
Ulusoy, Ayse and Tel, Banu Cahide and Elibol, Bülent},
title = {{A}utophagy activation ameliorates cognitive deficits and
alpha-synuclein pathology in an adeno-associated viral
vector mediated rat model of {L}ewy body disorders.},
journal = {Pharmacology, biochemistry and behavior},
volume = {257},
issn = {0091-3057},
address = {Amsterdam [u.a.]},
publisher = {Elsevier Science},
reportid = {DZNE-2025-01121},
pages = {174096},
year = {2025},
abstract = {Lewy body disorders (LBD), including Parkinson's disease
(PD), Parkinson's disease with dementia (PDD), and dementia
with Lewy bodies (DLB), are characterized by the aggregation
of alpha-synuclein (a-syn). Despite shared pathological
features, these disorders have distinct clinical
characteristics, in terms of both motor and cognitive
symptoms. We created a unique rat model of dual-site
injection of adeno-associated viral vectors carrying human
a-syn (AAV5-h-a-syn) simultaneously and bilaterally into the
substantia nigra and dentate gyrus, to recapitulate both
nigrostriatal and hippocampal-based a-syn pathology
associated with PDD and DLB. Inspired by the distinct
pathological features of the model, namely the CA2-dominated
accumulation of phosphorylated a-syn, in the current study
we aimed to evaluate comparatively the consequences of
autophagic induction on a-syn pathology in these targeted
areas. This was achieved by the chronic administration of
rapamycin, for 8 weeks starting 10 weeks post-AAV
injections. Behavioral assessments were conducted by
evaluation of locomotor activity, anxiety-related behavior,
object and spatial learning and memory. Histopathological
examinations involved in-depth analysis of a-syn pathology,
neuronal and synaptic integrity and autophagic markers.
Results demonstrated that rapamycin significantly
ameliorated cognitive deficits and reduced phosphorylated
a-syn accumulation, significantly in CA2 throughout all its
sublayers and partially in CA3 sublayers. Despite no
alteration in NeuN and TH levels, synaptophysin expressions
were decreased in both the hippocampus and striatum in a-syn
overexpressing animals, which were partially restored by
rapamycin treatment. Intriguingly, autophagic activation, as
indicated by the increased expression of beclin-1, LC3-I/II,
p62, and Atg proteins, was predominantly observed in the
hippocampus but not in the striatum, suggesting
region-specific differential response to autophagic
induction in terms of a-syn pathology. This dual-site
injection model provides a valuable tool for studying
a-syn-related dementia and evaluating potential restorative
therapies. Our findings underscore the importance of
autophagy-targeting early interventions to alleviate
cognitive deficits by reducing hippocampal a-syn burden in
LBD.},
keywords = {Animals / alpha-Synuclein: metabolism / alpha-Synuclein:
genetics / Autophagy: drug effects / Autophagy: physiology /
Rats / Dependovirus: genetics / Lewy Body Disease: pathology
/ Lewy Body Disease: metabolism / Lewy Body Disease:
psychology / Lewy Body Disease: therapy / Male / Disease
Models, Animal / Genetic Vectors / Cognitive Dysfunction:
therapy / Sirolimus: pharmacology / Humans / Rats,
Sprague-Dawley / Alpha-synucleinopathies (Other) / CA2
(Other) / Dementia (Other) / Hippocampus (Other) /
Parkinson's disease (Other) / Rapamycin (Other) / Stratum
pyramidale (Other) / Synaptic integrity (Other)},
cin = {AG Ulusoy},
ddc = {540},
cid = {I:(DE-2719)1013044},
pnm = {352 - Disease Mechanisms (POF4-352)},
pid = {G:(DE-HGF)POF4-352},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:40939811},
doi = {10.1016/j.pbb.2025.174096},
url = {https://pub.dzne.de/record/281436},
}