%0 Journal Article
%A Nagel, Gabriele
%A Peter, Raphael
%A Uzelac, Zeljko
%A Wernecke, Deborah
%A Niehaus, Ludwig
%A Trottenberg, Thomas
%A Jöbges, Michael
%A Dettmers, Christian
%A Bäzner, Hansjörg
%A Börtlein, Andreas
%A Althaus, Katharina
%A Mayer-Freitag, Kristina
%A Ratzka, Peter
%A Naumann, Markus
%A Lindner, Alfred
%A Chatzikonstantinou, Anastasios
%A Andres, Frank
%A Arnold, Guy
%A Blickhan, Marko
%A Opherk, Christian
%A Knier, Benjamin
%A Ertl, Michael
%A Metrikat, Jens
%A Huber, Roman
%A Thomas, Christine
%A Kozian, Ralf
%A Kimmig, Hubert
%A Demuth, Klaus
%A Hecht, Martin
%A Foerch, Christian
%A Kloetsch, Christof
%A Reinhard, Matthias
%A Bengel, Dietmar
%A Neuhaus, Oliver
%A Buttmann, Mathias
%A Volkmann, Jens
%A Pinkhardt, Elmar
%A Lichy, Christoph
%A Laske, Christoph
%A Beattie, James
%A Häckert, Jan
%A Jesse, Sarah
%A Brenner, David
%A Weishaupt, Jochen
%A Otto, Markus
%A Uttner, Ingo
%A Anderl-Straub, Sarah
%A Lule, Dorothee
%A Rothenbacher, Dietrich
%A Rosenbohm, Angela
%A Ludolph, Albert Christian
%T Incidence and Survival Rates of Frontotemporal Lobar Degeneration: Population-Based Registry Study.
%J Neurology
%V 106
%N 6
%@ 0028-3878
%C Philadelphia, Pa.
%I Wolters Kluwer
%M DZNE-2026-00214
%P e214482
%D 2026
%X Frontotemporal lobar degeneration (FTLD) can present as a behavioral or language variant (bvFTLD or a primary progressive aphasia [PPA], or as a syndrome with parkinsonism, such as corticobasal syndrome [CBS] or progressive supranuclear palsy [PSP]). The incidence of FTLD varies in epidemiologic studies, reaching 3 per 100,000 person-years. Only few data exist regarding survival times. We evaluated incidence and survival rates in a population-based registry with high coverage in Southern Germany.The epidemiologic ALS-FTLD registry Swabia covers a population of 8.4 million inhabitants in south-west Germany. Raw and age-standardized incidence rates, as well as incidence rate ratios (IRR) with 95
%K Humans
%K Male
%K Female
%K Registries
%K Incidence
%K Aged
%K Frontotemporal Lobar Degeneration: epidemiology
%K Frontotemporal Lobar Degeneration: mortality
%K Frontotemporal Lobar Degeneration: diagnosis
%K Middle Aged
%K Germany: epidemiology
%K Survival Rate
%K Aged, 80 and over
%F PUB:(DE-HGF)16
%9 Journal Article
%$ pmid:41730149
%R 10.1212/WNL.0000000000214482
%U https://pub.dzne.de/record/285348