TY  - JOUR
AU  - Nagel, Gabriele
AU  - Peter, Raphael
AU  - Uzelac, Zeljko
AU  - Wernecke, Deborah
AU  - Niehaus, Ludwig
AU  - Trottenberg, Thomas
AU  - Jöbges, Michael
AU  - Dettmers, Christian
AU  - Bäzner, Hansjörg
AU  - Börtlein, Andreas
AU  - Althaus, Katharina
AU  - Mayer-Freitag, Kristina
AU  - Ratzka, Peter
AU  - Naumann, Markus
AU  - Lindner, Alfred
AU  - Chatzikonstantinou, Anastasios
AU  - Andres, Frank
AU  - Arnold, Guy
AU  - Blickhan, Marko
AU  - Opherk, Christian
AU  - Knier, Benjamin
AU  - Ertl, Michael
AU  - Metrikat, Jens
AU  - Huber, Roman
AU  - Thomas, Christine
AU  - Kozian, Ralf
AU  - Kimmig, Hubert
AU  - Demuth, Klaus
AU  - Hecht, Martin
AU  - Foerch, Christian
AU  - Kloetsch, Christof
AU  - Reinhard, Matthias
AU  - Bengel, Dietmar
AU  - Neuhaus, Oliver
AU  - Buttmann, Mathias
AU  - Volkmann, Jens
AU  - Pinkhardt, Elmar
AU  - Lichy, Christoph
AU  - Laske, Christoph
AU  - Beattie, James
AU  - Häckert, Jan
AU  - Jesse, Sarah
AU  - Brenner, David
AU  - Weishaupt, Jochen
AU  - Otto, Markus
AU  - Uttner, Ingo
AU  - Anderl-Straub, Sarah
AU  - Lule, Dorothee
AU  - Rothenbacher, Dietrich
AU  - Rosenbohm, Angela
AU  - Ludolph, Albert Christian
TI  - Incidence and Survival Rates of Frontotemporal Lobar Degeneration: Population-Based Registry Study.
JO  - Neurology
VL  - 106
IS  - 6
SN  - 0028-3878
CY  - Philadelphia, Pa.
PB  - Wolters Kluwer
M1  - DZNE-2026-00214
SP  - e214482
PY  - 2026
AB  - Frontotemporal lobar degeneration (FTLD) can present as a behavioral or language variant (bvFTLD or a primary progressive aphasia [PPA], or as a syndrome with parkinsonism, such as corticobasal syndrome [CBS] or progressive supranuclear palsy [PSP]). The incidence of FTLD varies in epidemiologic studies, reaching 3 per 100,000 person-years. Only few data exist regarding survival times. We evaluated incidence and survival rates in a population-based registry with high coverage in Southern Germany.The epidemiologic ALS-FTLD registry Swabia covers a population of 8.4 million inhabitants in south-west Germany. Raw and age-standardized incidence rates, as well as incidence rate ratios (IRR) with 95
KW  - Humans
KW  - Male
KW  - Female
KW  - Registries
KW  - Incidence
KW  - Aged
KW  - Frontotemporal Lobar Degeneration: epidemiology
KW  - Frontotemporal Lobar Degeneration: mortality
KW  - Frontotemporal Lobar Degeneration: diagnosis
KW  - Middle Aged
KW  - Germany: epidemiology
KW  - Survival Rate
KW  - Aged, 80 and over
LB  - PUB:(DE-HGF)16
C6  - pmid:41730149
DO  - DOI:10.1212/WNL.0000000000214482
UR  - https://pub.dzne.de/record/285348
ER  -