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@ARTICLE{Ehninger:136241,
author = {Ehninger, Dan and Silva, Alcino J},
title = {{I}ncreased levels of anxiety-related behaviors in a {T}sc2
dominant negative transgenic mouse model of tuberous
sclerosis.},
journal = {Behavior genetics},
volume = {41},
number = {3},
issn = {0001-8244},
address = {Dordrecht [u.a.]},
publisher = {Springer Science + Business Media B.V},
reportid = {DZNE-2020-02563},
pages = {357-363},
year = {2011},
abstract = {Tuberous sclerosis (TSC) is a single-gene disorder caused
by heterozygous mutations in the TSC1 or TSC2 gene. TSC is
often associated with neurological (e.g., epilepsy),
cognitive (intellectual disabilities, specific
neuropsychological impairments) and behavioral pathologies
(e.g., autism, attention deficit hyperactivity disorder). In
addition, there is a high prevalence of psychiatric problems
in TSC populations, including anxiety and mood disorders. To
date, little is known about the pathogenetic bases of these
associated psychiatric symptoms; for instance, it is unclear
whether they are rooted in TSC-associated neurobiological
alterations or whether they are secondary psychological
phenomena (e.g., because individuals have to cope with the
burden of the disease). Here, we report elevated levels of
anxiety-related behaviors and mild deficits in two
hippocampal-dependent learning tasks in a Tsc2 dominant
negative transgenic mouse model of TSC. These findings
establish a mouse model for TSC-related anxiety phenotypes
and suggest that anxiety disorders in TSC have a biological
foundation.},
keywords = {Animals / Anxiety: genetics / Disease Models, Animal /
Female / Genes, Dominant: genetics / Genetic Carrier
Screening / Hippocampus: physiopathology / Humans / Learning
Disabilities: genetics / Learning Disabilities:
physiopathology / Male / Memory Disorders: genetics / Memory
Disorders: physiopathology / Mice / Mice, Inbred C57BL /
Mice, Transgenic / Phenotype / Tuberous Sclerosis: genetics
/ Tuberous Sclerosis: physiopathology / Tuberous Sclerosis
Complex 2 Protein / Tumor Suppressor Proteins: genetics /
TSC2 protein, human (NLM Chemicals) / Tsc2 protein, mouse
(NLM Chemicals) / Tuberous Sclerosis Complex 2 Protein (NLM
Chemicals) / Tumor Suppressor Proteins (NLM Chemicals)},
cin = {AG Ehninger},
ddc = {570},
cid = {I:(DE-2719)1013005},
pnm = {342 - Disease Mechanisms and Model Systems (POF3-342)},
pid = {G:(DE-HGF)POF3-342},
typ = {PUB:(DE-HGF)16},
pubmed = {pmid:20882401},
pmc = {pmc:PMC3102774},
doi = {10.1007/s10519-010-9398-1},
url = {https://pub.dzne.de/record/136241},
}